Scoliosis surgery in the Prader-Willi syndrome.
نویسندگان
چکیده
There is a high incidence of spinal deformity in children with the Prader-Willi syndrome. We have encountered major complications following spinal surgery in this condition. We report our experience and conclude that spinal surgery is a formidable undertaking and the risks should be appreciated by the surgeon and the parents.
منابع مشابه
Dental Management of Patients with Prader Willi Syndrome
Prader–Willi syndrome (PWS) is a genetic disorder which occurs with a frequency of about one in 10,000–30,000 live newborns. Both males and females, and all races are equally affected. PWS is a complex disorder with multiple disabilities, and the main defect is found in the hypothalamus. Child with PWS at the age between 2 and 3 years becomes constantly hungry and if the diet is not controlled,...
متن کاملScoliosis in Prader-Willi syndrome: prevalence, effects of age, gender, body mass index, lean body mass and genotype.
BACKGROUND The reported prevalence of scoliosis in children with Prader-Willi syndrome varies from 15% to 86%. OBJECTIVE To study the prevalence of scoliosis and the effects of age, gender, body mass index (BMI), total lean body mass (LBM), LBM of the trunk (trunkLBM) and genotype. DESIGN Radiographs were taken, length and weight were measured (BMI standard deviation scores (BMI SDS) and bo...
متن کاملScoliosis in patients with Prader Willi Syndrome – comparisons of conservative and surgical treatment
UNLABELLED In children with Prader Willi syndrome (PWS), besides growth hormone (GH) therapy, control of the food environment and regular exercise, surgical treatment of scoliosis deformities seems the treatment of choice, even though the risks of spinal surgery in this specific population is very high. Therefore the question arises as to whether the risks of spinal surgery outweigh the benefit...
متن کاملTreatment of scoliosis in patients affected with Prader-Willi syndrome using various techniques
BACKGROUND The incidence of spinal deformity in children with Prader-Willi syndrome (PWS) is high, with 86% of these patients found to have a significant structural scoliosis; however, there are very few case reports describing surgical treatment for this deformity. METHODS The authors reviewed a case series consisting of 6 patients who underwent spine surgery for scoliosis. Children's mean a...
متن کاملEffect of growth hormone on bone fragility in patients with Prader-Willi syndrome scoliosis
Objective Patients with Prader-Willi syndrome (PWS) is known to have bone fragility. Osteoporosis may be associated with bone fractures and poor surgical outcome for scoliosis. Current growth hormone (GH) treatment offers a viable and safe means to reduce these risks by improving bone density. The purposes of this study were to investigate bone mineral density (BMD) with PWS patients and to ver...
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ورودعنوان ژورنال:
- The Journal of bone and joint surgery. British volume
دوره 71 4 شماره
صفحات -
تاریخ انتشار 1989